Angiosarcoma in congenital hereditary lymphoedema (Milroy's disease) : diagnostic beacons and a review of the literature
Identifieur interne : 000D54 ( PascalFrancis/Corpus ); précédent : 000D53; suivant : 000D55Angiosarcoma in congenital hereditary lymphoedema (Milroy's disease) : diagnostic beacons and a review of the literature
Auteurs : T. W. Offori ; C. C. Platt ; M. Stephens ; G. B. HopkinsonSource :
- Clinical and experimental dermatology [ 0307-6938 ] ; 1993.
Descripteurs français
- Pascal (Inist)
English descriptors
- KwdEn :
Abstract
In cases of congenital lymphoedema the finding of ulceration, violaceous nodules or papules, or apparent traumatic ecchymoses1 should act as a diagnostic beacon warning of dangers. A case is reported of a high-grade angiosarcoma developing in a patient with congenital hereditary lymphoedema (Milroy's disease). This is the second paper to report this complication, the third case report and the first case in which the diagnosis is substantiated by immunohistochemistry and lectin histochemistry. A review of cases of angiosarcoma complicating congenital hereditary and non-hereditary lymphoedema is also presented
Notice en format standard (ISO 2709)
Pour connaître la documentation sur le format Inist Standard.
pA |
|
---|
Format Inist (serveur)
NO : | PASCAL 93-0352233 INIST |
---|---|
ET : | Angiosarcoma in congenital hereditary lymphoedema (Milroy's disease) : diagnostic beacons and a review of the literature |
AU : | OFFORI (T. W.); PLATT (C. C.); STEPHENS (M.); HOPKINSON (G. B.) |
AF : | North Staffordshire hosp. cent., dep. surgery/Stroke-on-Trent/Royaume-Uni (1 aut., 4 aut.) |
DT : | Publication en série; Etude de cas, cas et faits cliniques; Niveau analytique |
SO : | Clinical and experimental dermatology; ISSN 0307-6938; Coden CEDEDE; Royaume-Uni; Da. 1993; Vol. 18; No. 2; Pp. 174-177; Bibl. 20 ref. |
LA : | Anglais |
EA : | In cases of congenital lymphoedema the finding of ulceration, violaceous nodules or papules, or apparent traumatic ecchymoses1 should act as a diagnostic beacon warning of dangers. A case is reported of a high-grade angiosarcoma developing in a patient with congenital hereditary lymphoedema (Milroy's disease). This is the second paper to report this complication, the third case report and the first case in which the diagnosis is substantiated by immunohistochemistry and lectin histochemistry. A review of cases of angiosarcoma complicating congenital hereditary and non-hereditary lymphoedema is also presented |
CC : | 002B12B04 |
FD : | Lymphoedème; Angiosarcome; Congénital; Complication; Diagnostic; Immunohistochimie; Histochimie; Anatomopathologie; Exploration; Etude cas |
FG : | Appareil circulatoire pathologie; Lymphatique pathologie; Peau pathologie; Maladie congénitale; Vaisseau sanguin pathologie; Tumeur maligne; Homme; Femelle |
ED : | Lymphedema; Angiosarcoma; Congenital; Complication; Diagnosis; Immunohistochemistry; Histochemistry; Pathology; Exploration; Case study |
EG : | Cardiovascular disease; Lymphatic vessel disease; Skin disease; Congenital disease; Vascular disease; Malignant tumor; Human; Female |
SD : | Linfedema; Angiosarcoma; Congénito; Complicación; Diagnóstico; Inmunohistoquímica; Histoquímica; Anatomía patológica; Exploración; Estudio caso |
LO : | INIST-16224.354000037105150240 |
ID : | 93-0352233 |
Links to Exploration step
Pascal:93-0352233Le document en format XML
<record><TEI><teiHeader><fileDesc><titleStmt><title xml:lang="en" level="a">Angiosarcoma in congenital hereditary lymphoedema (Milroy's disease) : diagnostic beacons and a review of the literature</title>
<author><name sortKey="Offori, T W" sort="Offori, T W" uniqKey="Offori T" first="T. W." last="Offori">T. W. Offori</name>
<affiliation><inist:fA14 i1="01"><s1>North Staffordshire hosp. cent., dep. surgery</s1>
<s2>Stroke-on-Trent</s2>
<s3>GBR</s3>
<sZ>1 aut.</sZ>
<sZ>4 aut.</sZ>
</inist:fA14>
</affiliation>
</author>
<author><name sortKey="Platt, C C" sort="Platt, C C" uniqKey="Platt C" first="C. C." last="Platt">C. C. Platt</name>
</author>
<author><name sortKey="Stephens, M" sort="Stephens, M" uniqKey="Stephens M" first="M." last="Stephens">M. Stephens</name>
</author>
<author><name sortKey="Hopkinson, G B" sort="Hopkinson, G B" uniqKey="Hopkinson G" first="G. B." last="Hopkinson">G. B. Hopkinson</name>
<affiliation><inist:fA14 i1="01"><s1>North Staffordshire hosp. cent., dep. surgery</s1>
<s2>Stroke-on-Trent</s2>
<s3>GBR</s3>
<sZ>1 aut.</sZ>
<sZ>4 aut.</sZ>
</inist:fA14>
</affiliation>
</author>
</titleStmt>
<publicationStmt><idno type="wicri:source">INIST</idno>
<idno type="inist">93-0352233</idno>
<date when="1993">1993</date>
<idno type="stanalyst">PASCAL 93-0352233 INIST</idno>
<idno type="RBID">Pascal:93-0352233</idno>
<idno type="wicri:Area/PascalFrancis/Corpus">000D54</idno>
</publicationStmt>
<sourceDesc><biblStruct><analytic><title xml:lang="en" level="a">Angiosarcoma in congenital hereditary lymphoedema (Milroy's disease) : diagnostic beacons and a review of the literature</title>
<author><name sortKey="Offori, T W" sort="Offori, T W" uniqKey="Offori T" first="T. W." last="Offori">T. W. Offori</name>
<affiliation><inist:fA14 i1="01"><s1>North Staffordshire hosp. cent., dep. surgery</s1>
<s2>Stroke-on-Trent</s2>
<s3>GBR</s3>
<sZ>1 aut.</sZ>
<sZ>4 aut.</sZ>
</inist:fA14>
</affiliation>
</author>
<author><name sortKey="Platt, C C" sort="Platt, C C" uniqKey="Platt C" first="C. C." last="Platt">C. C. Platt</name>
</author>
<author><name sortKey="Stephens, M" sort="Stephens, M" uniqKey="Stephens M" first="M." last="Stephens">M. Stephens</name>
</author>
<author><name sortKey="Hopkinson, G B" sort="Hopkinson, G B" uniqKey="Hopkinson G" first="G. B." last="Hopkinson">G. B. Hopkinson</name>
<affiliation><inist:fA14 i1="01"><s1>North Staffordshire hosp. cent., dep. surgery</s1>
<s2>Stroke-on-Trent</s2>
<s3>GBR</s3>
<sZ>1 aut.</sZ>
<sZ>4 aut.</sZ>
</inist:fA14>
</affiliation>
</author>
</analytic>
<series><title level="j" type="main">Clinical and experimental dermatology</title>
<title level="j" type="abbreviated">Clin. exp. dermatol.</title>
<idno type="ISSN">0307-6938</idno>
<imprint><date when="1993">1993</date>
</imprint>
</series>
</biblStruct>
</sourceDesc>
<seriesStmt><title level="j" type="main">Clinical and experimental dermatology</title>
<title level="j" type="abbreviated">Clin. exp. dermatol.</title>
<idno type="ISSN">0307-6938</idno>
</seriesStmt>
</fileDesc>
<profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Angiosarcoma</term>
<term>Case study</term>
<term>Complication</term>
<term>Congenital</term>
<term>Diagnosis</term>
<term>Exploration</term>
<term>Histochemistry</term>
<term>Immunohistochemistry</term>
<term>Lymphedema</term>
<term>Pathology</term>
</keywords>
<keywords scheme="Pascal" xml:lang="fr"><term>Lymphoedème</term>
<term>Angiosarcome</term>
<term>Congénital</term>
<term>Complication</term>
<term>Diagnostic</term>
<term>Immunohistochimie</term>
<term>Histochimie</term>
<term>Anatomopathologie</term>
<term>Exploration</term>
<term>Etude cas</term>
</keywords>
</textClass>
</profileDesc>
</teiHeader>
<front><div type="abstract" xml:lang="en">In cases of congenital lymphoedema the finding of ulceration, violaceous nodules or papules, or apparent traumatic ecchymoses<sup>1</sup>
should act as a diagnostic beacon warning of dangers. A case is reported of a high-grade angiosarcoma developing in a patient with congenital hereditary lymphoedema (Milroy's disease). This is the second paper to report this complication, the third case report and the first case in which the diagnosis is substantiated by immunohistochemistry and lectin histochemistry. A review of cases of angiosarcoma complicating congenital hereditary and non-hereditary lymphoedema is also presented</div>
</front>
</TEI>
<inist><standard h6="B"><pA><fA01 i1="01" i2="1"><s0>0307-6938</s0>
</fA01>
<fA02 i1="01"><s0>CEDEDE</s0>
</fA02>
<fA03 i2="1"><s0>Clin. exp. dermatol.</s0>
</fA03>
<fA05><s2>18</s2>
</fA05>
<fA06><s2>2</s2>
</fA06>
<fA08 i1="01" i2="1" l="ENG"><s1>Angiosarcoma in congenital hereditary lymphoedema (Milroy's disease) : diagnostic beacons and a review of the literature</s1>
</fA08>
<fA11 i1="01" i2="1"><s1>OFFORI (T. W.)</s1>
</fA11>
<fA11 i1="02" i2="1"><s1>PLATT (C. C.)</s1>
</fA11>
<fA11 i1="03" i2="1"><s1>STEPHENS (M.)</s1>
</fA11>
<fA11 i1="04" i2="1"><s1>HOPKINSON (G. B.)</s1>
</fA11>
<fA14 i1="01"><s1>North Staffordshire hosp. cent., dep. surgery</s1>
<s2>Stroke-on-Trent</s2>
<s3>GBR</s3>
<sZ>1 aut.</sZ>
<sZ>4 aut.</sZ>
</fA14>
<fA20><s1>174-177</s1>
</fA20>
<fA21><s1>1993</s1>
</fA21>
<fA23 i1="01"><s0>ENG</s0>
</fA23>
<fA43 i1="01"><s1>INIST</s1>
<s2>16224</s2>
<s5>354000037105150240</s5>
</fA43>
<fA44><s0>0000</s0>
</fA44>
<fA45><s0>20 ref.</s0>
</fA45>
<fA47 i1="01" i2="1"><s0>93-0352233</s0>
</fA47>
<fA60><s1>P</s1>
<s3>EC</s3>
</fA60>
<fA61><s0>A</s0>
</fA61>
<fA64 i2="1"><s0>Clinical and experimental dermatology</s0>
</fA64>
<fA66 i1="01"><s0>GBR</s0>
</fA66>
<fC01 i1="01" l="ENG"><s0>In cases of congenital lymphoedema the finding of ulceration, violaceous nodules or papules, or apparent traumatic ecchymoses<sup>1</sup>
should act as a diagnostic beacon warning of dangers. A case is reported of a high-grade angiosarcoma developing in a patient with congenital hereditary lymphoedema (Milroy's disease). This is the second paper to report this complication, the third case report and the first case in which the diagnosis is substantiated by immunohistochemistry and lectin histochemistry. A review of cases of angiosarcoma complicating congenital hereditary and non-hereditary lymphoedema is also presented</s0>
</fC01>
<fC02 i1="01" i2="X"><s0>002B12B04</s0>
</fC02>
<fC03 i1="01" i2="X" l="FRE"><s0>Lymphoedème</s0>
<s2>NM</s2>
<s2>L1</s2>
</fC03>
<fC03 i1="01" i2="X" l="ENG"><s0>Lymphedema</s0>
<s2>NM</s2>
<s2>L1</s2>
</fC03>
<fC03 i1="01" i2="X" l="SPA"><s0>Linfedema</s0>
<s2>NM</s2>
<s2>L1</s2>
</fC03>
<fC03 i1="02" i2="X" l="FRE"><s0>Angiosarcome</s0>
<s2>NM</s2>
</fC03>
<fC03 i1="02" i2="X" l="ENG"><s0>Angiosarcoma</s0>
<s2>NM</s2>
</fC03>
<fC03 i1="02" i2="X" l="SPA"><s0>Angiosarcoma</s0>
<s2>NM</s2>
</fC03>
<fC03 i1="03" i2="X" l="FRE"><s0>Congénital</s0>
<s2>L1</s2>
</fC03>
<fC03 i1="03" i2="X" l="ENG"><s0>Congenital</s0>
<s2>L1</s2>
</fC03>
<fC03 i1="03" i2="X" l="SPA"><s0>Congénito</s0>
<s2>L1</s2>
</fC03>
<fC03 i1="04" i2="X" l="FRE"><s0>Complication</s0>
</fC03>
<fC03 i1="04" i2="X" l="ENG"><s0>Complication</s0>
</fC03>
<fC03 i1="04" i2="X" l="SPA"><s0>Complicación</s0>
</fC03>
<fC03 i1="05" i2="X" l="FRE"><s0>Diagnostic</s0>
</fC03>
<fC03 i1="05" i2="X" l="ENG"><s0>Diagnosis</s0>
</fC03>
<fC03 i1="05" i2="X" l="SPA"><s0>Diagnóstico</s0>
</fC03>
<fC03 i1="06" i2="X" l="FRE"><s0>Immunohistochimie</s0>
</fC03>
<fC03 i1="06" i2="X" l="ENG"><s0>Immunohistochemistry</s0>
</fC03>
<fC03 i1="06" i2="X" l="SPA"><s0>Inmunohistoquímica</s0>
</fC03>
<fC03 i1="07" i2="X" l="FRE"><s0>Histochimie</s0>
</fC03>
<fC03 i1="07" i2="X" l="ENG"><s0>Histochemistry</s0>
</fC03>
<fC03 i1="07" i2="X" l="SPA"><s0>Histoquímica</s0>
</fC03>
<fC03 i1="08" i2="X" l="FRE"><s0>Anatomopathologie</s0>
</fC03>
<fC03 i1="08" i2="X" l="ENG"><s0>Pathology</s0>
</fC03>
<fC03 i1="08" i2="X" l="SPA"><s0>Anatomía patológica</s0>
</fC03>
<fC03 i1="09" i2="X" l="FRE"><s0>Exploration</s0>
</fC03>
<fC03 i1="09" i2="X" l="ENG"><s0>Exploration</s0>
</fC03>
<fC03 i1="09" i2="X" l="SPA"><s0>Exploración</s0>
</fC03>
<fC03 i1="10" i2="X" l="FRE"><s0>Etude cas</s0>
</fC03>
<fC03 i1="10" i2="X" l="ENG"><s0>Case study</s0>
</fC03>
<fC03 i1="10" i2="X" l="SPA"><s0>Estudio caso</s0>
</fC03>
<fC07 i1="01" i2="X" l="FRE"><s0>Appareil circulatoire pathologie</s0>
</fC07>
<fC07 i1="01" i2="X" l="ENG"><s0>Cardiovascular disease</s0>
</fC07>
<fC07 i1="01" i2="X" l="SPA"><s0>Aparato circulatorio patología</s0>
</fC07>
<fC07 i1="02" i2="X" l="FRE"><s0>Lymphatique pathologie</s0>
</fC07>
<fC07 i1="02" i2="X" l="ENG"><s0>Lymphatic vessel disease</s0>
</fC07>
<fC07 i1="02" i2="X" l="SPA"><s0>Linfático patología</s0>
</fC07>
<fC07 i1="03" i2="X" l="FRE"><s0>Peau pathologie</s0>
</fC07>
<fC07 i1="03" i2="X" l="ENG"><s0>Skin disease</s0>
</fC07>
<fC07 i1="03" i2="X" l="SPA"><s0>Piel patología</s0>
</fC07>
<fC07 i1="04" i2="X" l="FRE"><s0>Maladie congénitale</s0>
</fC07>
<fC07 i1="04" i2="X" l="ENG"><s0>Congenital disease</s0>
</fC07>
<fC07 i1="04" i2="X" l="SPA"><s0>Enfermedad congénita</s0>
</fC07>
<fC07 i1="05" i2="X" l="FRE"><s0>Vaisseau sanguin pathologie</s0>
</fC07>
<fC07 i1="05" i2="X" l="ENG"><s0>Vascular disease</s0>
</fC07>
<fC07 i1="05" i2="X" l="SPA"><s0>Vaso sanguíneo patología</s0>
</fC07>
<fC07 i1="06" i2="X" l="FRE"><s0>Tumeur maligne</s0>
</fC07>
<fC07 i1="06" i2="X" l="ENG"><s0>Malignant tumor</s0>
</fC07>
<fC07 i1="06" i2="X" l="SPA"><s0>Tumor maligno</s0>
</fC07>
<fC07 i1="07" i2="X" l="FRE"><s0>Homme</s0>
</fC07>
<fC07 i1="07" i2="X" l="ENG"><s0>Human</s0>
</fC07>
<fC07 i1="07" i2="X" l="SPA"><s0>Hombre</s0>
</fC07>
<fC07 i1="08" i2="X" l="FRE"><s0>Femelle</s0>
</fC07>
<fC07 i1="08" i2="X" l="ENG"><s0>Female</s0>
</fC07>
<fC07 i1="08" i2="X" l="SPA"><s0>Hembra</s0>
</fC07>
<fN21><s1>132</s1>
</fN21>
</pA>
</standard>
<server><NO>PASCAL 93-0352233 INIST</NO>
<ET>Angiosarcoma in congenital hereditary lymphoedema (Milroy's disease) : diagnostic beacons and a review of the literature</ET>
<AU>OFFORI (T. W.); PLATT (C. C.); STEPHENS (M.); HOPKINSON (G. B.)</AU>
<AF>North Staffordshire hosp. cent., dep. surgery/Stroke-on-Trent/Royaume-Uni (1 aut., 4 aut.)</AF>
<DT>Publication en série; Etude de cas, cas et faits cliniques; Niveau analytique</DT>
<SO>Clinical and experimental dermatology; ISSN 0307-6938; Coden CEDEDE; Royaume-Uni; Da. 1993; Vol. 18; No. 2; Pp. 174-177; Bibl. 20 ref.</SO>
<LA>Anglais</LA>
<EA>In cases of congenital lymphoedema the finding of ulceration, violaceous nodules or papules, or apparent traumatic ecchymoses<sup>1</sup>
should act as a diagnostic beacon warning of dangers. A case is reported of a high-grade angiosarcoma developing in a patient with congenital hereditary lymphoedema (Milroy's disease). This is the second paper to report this complication, the third case report and the first case in which the diagnosis is substantiated by immunohistochemistry and lectin histochemistry. A review of cases of angiosarcoma complicating congenital hereditary and non-hereditary lymphoedema is also presented</EA>
<CC>002B12B04</CC>
<FD>Lymphoedème; Angiosarcome; Congénital; Complication; Diagnostic; Immunohistochimie; Histochimie; Anatomopathologie; Exploration; Etude cas</FD>
<FG>Appareil circulatoire pathologie; Lymphatique pathologie; Peau pathologie; Maladie congénitale; Vaisseau sanguin pathologie; Tumeur maligne; Homme; Femelle</FG>
<ED>Lymphedema; Angiosarcoma; Congenital; Complication; Diagnosis; Immunohistochemistry; Histochemistry; Pathology; Exploration; Case study</ED>
<EG>Cardiovascular disease; Lymphatic vessel disease; Skin disease; Congenital disease; Vascular disease; Malignant tumor; Human; Female</EG>
<SD>Linfedema; Angiosarcoma; Congénito; Complicación; Diagnóstico; Inmunohistoquímica; Histoquímica; Anatomía patológica; Exploración; Estudio caso</SD>
<LO>INIST-16224.354000037105150240</LO>
<ID>93-0352233</ID>
</server>
</inist>
</record>
Pour manipuler ce document sous Unix (Dilib)
EXPLOR_STEP=$WICRI_ROOT/Wicri/Sante/explor/LymphedemaV1/Data/PascalFrancis/Corpus
HfdSelect -h $EXPLOR_STEP/biblio.hfd -nk 000D54 | SxmlIndent | more
Ou
HfdSelect -h $EXPLOR_AREA/Data/PascalFrancis/Corpus/biblio.hfd -nk 000D54 | SxmlIndent | more
Pour mettre un lien sur cette page dans le réseau Wicri
{{Explor lien |wiki= Wicri/Sante |area= LymphedemaV1 |flux= PascalFrancis |étape= Corpus |type= RBID |clé= Pascal:93-0352233 |texte= Angiosarcoma in congenital hereditary lymphoedema (Milroy's disease) : diagnostic beacons and a review of the literature }}
This area was generated with Dilib version V0.6.31. |